Cystic Fibrosis in Children: Board Questions

What this deck covers

Cystic Fibrosis in 18 board-style clinical cases with worked explanations. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong, with the guideline or textbook it follows named on the answer.

Board-style teaching questions for paediatricians and trainees preparing for board, MRCPCH and Prometric examinations. Written from published guidelines and standard paediatric textbooks, with the source named on every answer.

The 18 cases, in order

1. An abnormal spot in a well baby
2. But his newborn test was clear
3. What about the next baby
4. Nothing passed in thirty-six hours
5. First growth on a routine swab
6. Same bug for two years
7. Why is he on antibiotics at all
8. Can he still go to camp
9. Two antibiotics and still worse
10. Losing weight despite doing everything
11. A lump in the right iliac fossa
12. Both nostrils blocked for a year
13. Floppy in the heatwave
14. What happens every day at home
15. The drug they read about
16. Will he be able to have children
17. No fever but the numbers fell
18. Two children, one afternoon

Diagnoses and management options tested

Across the 18 cases you are asked to choose between options such as: One in four, Meconium ileus, Measurement of glycated haemoglobin, Acute appendicitis, Enlarged adenoids, A daily oral antihistamine.

Clinical pearls from this deck

• A well baby is what a positive screen looks like. Do not let it slow the referral.
• A negative screen is a probability, not a verdict. The symptoms outrank it.
• No family history is the normal presentation. Carriers are common and perfectly well.
• Meconium ileus is a diagnosis of the whole child, not of the bowel. Chase the cause every time.
• Surveillance swabs exist to catch the first isolate. Treating it is the whole reason they are taken.
• Eradicate the first isolate. Suppress the chronic one. Confusing the two wastes years.

Work through the deck once for recognition, then again a week later to test yourself — each question gives the answer and explains why every other option fails.

More from this system: all Respiratory Board Questions case decks · pediatric reference values.