Hypertrophic Cardiomyopathy – Board-Style Questions

What this deck covers

hypertrophic cardiomyopathy in 18 board-style clinical cases with worked explanations. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong, with the guideline or textbook it follows named on the answer.

Board-style teaching questions for paediatricians and trainees preparing for paediatric board, MRCPCH and licensing examinations. Written from published guidelines and standard paediatric textbooks, with the source named on every answer.

The 18 cases, in order

1. How it is inherited
2. The ECG
3. Who is at risk
4. Preventing sudden death
5. First treatment
6. What to avoid
7. When medicines fail
8. A neurological clue
9. Athlete or disease
10. His daughter
11. Gene positive, heart normal
12. An irregular pulse
13. The cause of obstruction
14. In pregnancy
15. Looking for arrhythmia
16. Chest pain
17. Estimating risk
18. Revision season

Diagnoses and management options tested

Across the 18 cases you are asked to choose between options such as: Recessive variants needing two copies from each parent in turn, Marked left ventricular hypertrophy with deep T inversion, It is normal for his age, A higher dose of beta blocker alone, Beta blockade to lengthen filling time, Give the vasodilator as planned, Increase to a higher dose, Duchenne muscular dystrophy, Wall thickness falling after stopping training, Whole genome sequencing of every gene, Discharge, as his heart is normal, No anticoagulation, as her usual stroke score is zero, Systolic anterior motion of the mitral valve, Stop the beta blocker at once and review.

Clinical pearls from this deck

• Familial HCM comes from dominant sarcomere variants.
• HCM on the ECG: big voltages and deep T wave inversion.
• A massive wall thickness means a high risk of sudden death.
• In high-risk HCM, an implanted defibrillator saves lives.
• Symptoms from obstruction: start with a beta blocker.
• With obstruction, keep him filled and avoid vasodilators.

Work through the deck once for recognition, then again a week later to test yourself — each question gives the answer and explains why every other option fails.

More from this system: all cardiology case decks · pediatric reference values.