Pulmonary Atresia with Intact Ventricular Septum – Board-Style Questions

What this deck covers

pulmonary atresia with intact ventricular septum in 18 board-style clinical cases with worked explanations. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong, with the guideline or textbook it follows named on the answer.

Board-style teaching questions for paediatricians and trainees preparing for paediatric board, MRCPCH and licensing examinations. Written from published guidelines and standard paediatric textbooks, with the source named on every answer.

The 18 cases, in order

1. The deciding measurement
2. A dangerous connection
3. What not to do
4. Opening the valve
5. Still blue
6. Predicting the route
7. Before any procedure
8. Tiny chamber
9. In between
10. The chest film
11. Not just stenosis
12. Talking about the future
13. Before birth
14. Bigger each time
15. Supporting lung flow
16. The best case
17. Trouble after the wire
18. Is it finished

Diagnoses and management options tested

Across the 18 cases you are asked to choose between options such as: The size of the left atrium, Part of the muscle is fed from the ventricle, Open the valve urgently with a balloon, A Fontan operation in the first week, A duct stent or shunt for extra lung flow, It shows whether he has a murmur, A brain MRI to look for bleeding, A two-ventricle repair, A one-and-a-half ventricle repair, White-out of both lungs, A thin jet across the valve, His birth weight and gestation, Fetal balloon valvuloplasty, Heart failure from too much fluid.

Clinical pearls from this deck

• PA-IVS: the tricuspid valve and right ventricle decide the path.
• Sinusoids with coronary narrowing: RV-dependent coronaries.
• RV-dependent coronaries: do not decompress.
• Good right ventricle, thin membrane: perforate and balloon.
• Still blue after perforation: add lung flow.
• Measure the tricuspid valve to plan the route.

Work through the deck once for recognition, then again a week later to test yourself — each question gives the answer and explains why every other option fails.

More from this system: all cardiology case decks · pediatric reference values.