Bronchiectasis and Primary Ciliary Dyskinesia

What this deck covers

Bronchiectasis and Primary Ciliary Dyskinesia in twelve board-style clinical cases with worked explanations, written for the Saudi Prometric (SCFHS) exam, MRCPCH Part 1 and Part 2, the Arab Board, DHA and OMSB. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong.

The 12 cases, in order

1. The cough that never quite clears
2. The same cough, two diseases
3. What the scan has to show
4. Now find out why
5. The clue in the newborn notes
6. Which way round is he
7. Proving it
8. The treatment that does the most
9. When the cough changes
10. Watching the long game
11. The ears are part of it
12. The conversation about later

Diagnoses and management options tested

Across the twelve cases you are asked to choose between options such as: Two viral colds during the winter, Ground-glass opacification of both lower lobes, Air trapping on the expiratory sequence, Smooth thickening of the pleura, Record it as post-infectious and treat symptomatically, A family history of asthma and eczema, Isolated dextrocardia with otherwise normal anatomy, A congenital diaphragmatic hernia displacing the heart, Situs inversus totalis, completing the Kartagener triad, A negative genetic panel excludes the condition, Daily airway clearance physiotherapy, A regular inhaled corticosteroid, Nebulised dornase alfa, A continuous low-dose oral corticosteroid.

Exam pearls from this deck

• Four weeks of a wet cough earns a two-week targeted antibiotic. What happens after that course is the diagnostic test.
• Both start as a wet cough. What separates them is the child between the episodes, not during them.
• An airway wider than the artery beside it is the signet ring. That ratio is the diagnosis.
• Bronchiectasis is a finding, not a diagnosis. Every child gets a search for a cause.
• Unexplained respiratory distress in a term newborn, with year-round nasal symptoms from infancy, is ciliary dyskinesia until it is excluded.
• Mirror image of heart and stomach together, with bronchiectasis and sinusitis, is the Kartagener triad. It appears in about half of ciliary dyskinesia.

The deck above is free and needs no sign-in. Work through it once for recognition, then again a week later for recall — the questions are written in the format the exam actually uses.

More from this system: all respiratory decks and question sets · the free Pediatric Prometric question bank · pediatric reference values.