What this deck covers
Congenital and Acquired Hearing Loss in ten clinical teaching cases with worked explanations. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong.
Diagnoses and management options tested
Across the ten cases you are asked to choose between options such as: Permanent sensorineural hearing loss from bacterial toxins, Ossicular discontinuity from infection, Tympanic membrane perforation with ossicular damage, Immediate tympanostomy tube placement, Watchful waiting with audiological monitoring, Adenoidectomy and tympanostomy tubes, Genetic testing for hereditary hearing loss, Autosomal dominant with incomplete penetrance, Autosomal recessive, X-linked recessive, Mitochondrial inheritance with maternal transmission, Jervell and Lange-Nielsen syndrome, Usher syndrome, Waardenburg syndrome, Pendred syndrome, Administer sodium thiosulfate before each cisplatin dose, Ossicular fixation from abnormal bone development, Tympanic membrane perforation from recurrent infection, Sensorineural loss from inner ear malformation.
Clinical pearls from this deck
- A failed newborn screen — especially after a confirmatory repeat — needs prompt referral to a pediatric audiologist, not reassurance or more screening. The startle reflex is unreliable (infants react to vibration/visual/loud cues even with significant SNHL). Follow the 1-3-6 rule: screen by 1 month, diagnose by 3 months, intervene by 6 months. Imaging is reserved for confirmed SNHL.
- Congenital CMV is the leading NON-genetic cause of pediatric SNHL (~20–30% of congenital hearing loss). Crucially, CMV loss can be delayed-onset and progressive — a child may pass the newborn screen and lose hearing over the next few years. So every congenital-CMV infant (even asymptomatic) needs serial audiology (every 3–6 months in year 1, then 6–12 monthly to ~age 6). Valganciclovir in the first month may reduce progression in symptomatic infants.
The ten worked cases in this deck, with the images and the full explanation of every option, are part of Pediatric Case Review membership. See what is included.
More from this system: all ent decks and question sets · pediatric reference values.
