Cystic Fibrosis

What this deck covers

Cystic Fibrosis in twelve clinical teaching cases with worked explanations. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong.

The 12 cases, in order

1. A telephone call from screening
2. The test in the laboratory
3. What cftr was doing
4. Weight in the clinic
5. A newborn on the postnatal ward
6. A routine cough swab
7. The scan at annual review
8. A call from the family
9. A sign at the bedside
10. A blocked nose in clinic
11. Beyond the lung
12. A question in the waiting room

Diagnoses and management options tested

Across the twelve cases you are asked to choose between options such as: Hirschsprung disease; arrange a suction rectal biopsy, Emphysema, from destruction of the alveolar walls, Bronchiectasis — irreversible dilatation of the airway, Drug-induced hepatitis from long-term azithromycin.

Clinical pearls from this deck

• CFTR secretes chloride and bicarbonate; without it the surface liquid loses its water.
• Around eighty-five per cent of children with cystic fibrosis are pancreatically insufficient.

The twelve worked cases in this deck, with the images and the full explanation of every option, are part of Pediatric Case Review membership. See what is included.

More from this system: all respiratory decks and question sets · pediatric reference values.