Bronchiectasis and Primary Ciliary Dyskinesia in Children: Board Questions

What this deck covers

Bronchiectasis and Primary Ciliary Dyskinesia in 18 board-style clinical cases with worked explanations. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong, with the guideline or textbook it follows named on the answer.

Board-style teaching questions for paediatricians and trainees preparing for board, MRCPCH and Prometric examinations. Written from published guidelines and standard paediatric textbooks, with the source named on every answer.

The 18 cases, in order

1. Two years of morning sputum
2. Is this permanent
3. Finding out why it happened
4. Snuffly since the day he was born
5. Heart on the wrong side
6. A quick test before referral
7. Glue ear that will not clear
8. Will he be able to have children
9. Meningitis, ears and a joint
10. Ever since that one pneumonia
11. What matters most every day
12. Thicker, greener, and weaker
13. Five flare-ups this year
14. What the sputum usually grows
15. Something before the winter
16. When an operation is worth it
17. How to follow him over years
18. What his life will look like

Diagnoses and management options tested

Across the 18 cases you are asked to choose between options such as: A thin-section computed tomography scan of the chest, A systematic search for a treatable underlying cause, Primary ciliary dyskinesia, Reversed organ arrangement, Measurement of nitric oxide sampled from the nose, Long-term azithromycin taken on three days a week, Staphylococcus aureus, Surgical removal of the affected lobe.

Clinical pearls from this deck

• A film reported as increased markings in a child with daily sputum is a normal-looking failure.
• Say early that it can improve. Families arrive believing they have been given a life sentence.
• It is a finding, not a diagnosis. Two thirds of these children have a reason worth finding.
• Ask when the runny nose started. From day one is a different disease from from six months.
• Look at where the heart and the liver are. Half of these children hand you the diagnosis.
• Nose low, not chest. Two nitric oxide tests exist and they answer opposite questions.

Work through the deck once for recognition, then again a week later to test yourself — each question gives the answer and explains why every other option fails.

More from this system: all Respiratory Board Questions case decks · pediatric reference values.