Capillary Malformation and Sturge-Weber Syndrome – Board-Style Questions

What this deck covers

Capillary malformation and Sturge-Weber syndrome in 18 board-style clinical cases with worked explanations. Each case gives you a clinical vignette, four options, the correct answer, and an explanation of why each of the other three is wrong, with the guideline or textbook it follows named on the answer.

Board-style teaching questions for paediatricians and trainees preparing for paediatric board, MRCPCH and licensing examinations. Written from published guidelines and standard paediatric textbooks, with the source named on every answer.

The 18 cases, in order

1. Fading by the fourth birthday
2. The mark that stays
3. Where it sits matters
4. What the scan shows
5. Watching the eye
6. The next baby
7. The first fit
8. Lines on the film
9. The limb that grew
10. Turning down the red
11. Why the weakness comes
12. How often to look
13. What lies ahead
14. Bumping into things
15. As the years pass
16. When drugs are not enough
17. The bad headaches
18. More than the skin

Diagnoses and management options tested

Across the 18 cases you are asked to choose between options such as: An infantile haemangioma at the start of growth, A capillary malformation, which persists lifelong, The chin and the lower lip, in a mandibular pattern, Thickening of the skull bones on that side, Glaucoma of the eye under the birthmark, An autosomal dominant condition from one parent, A simple febrile seizure needing no further tests, Old bleeding from the injury she has just had, Klippel-Trenaunay syndrome of the left leg, Surgical excision and a split skin graft, Inflammation of arteries in the neck, Once more at one year and then no further checks, Fits usually begin in the first two years, A squint that has not yet been corrected.

Clinical pearls from this deck

• Midline pink patch that blanches: naevus simplex.
• Sharp, segmental, present at birth: it is there for life.
• Upper face involved: the brain and eye are at risk.
• Contrast lighting up one hemisphere: the brain is involved.
• Big watery eye under the birthmark: check the pressure.
• It arises after conception, so parents are not carriers.

Work through the deck once for recognition, then again a week later to test yourself — each question gives the answer and explains why every other option fails.

More from this system: all dermatology case decks · pediatric reference values.